Síndrome de Wilkie a propósito de un caso

Abstract

Introduction: Known Wilkie syndrome is considered a rare cause of proximal obstruction of the small intestine, which can be partial or total. In humans, the aortomesenteric angle varies from 38° to 65° due to upright posture; the normal aortomesenteric distance is 10 and 28mm. The main anatomical characteristic of Wilkie syndrome is the narrowing of the aortomesenteric angle to <25°, consequently, there is a decrease in the aortomesenteric distance of <10mm. The estimated incidence is 0.1% to 0.3% in the general population and in pediatric patients it is 0.01%. The etiology is multifactorial, it is related to sudden weight loss, which decreases retroperitoneal fatty tissue. Objectives: To define the diagnosis and timely management in pediatric patients with Wilkie syndrome. Materials and methods: A cross-sectional descriptive study based on clinical case analysis is carried out. Conclusion: Wilkie syndrome is a disease that is difficult to diagnose due to its low incidence and nonspecific symptoms. It is suspected in cases of severe weight loss and upper digestive symptoms. Computerized axial tomography is considered the gold standard and should be used whenever the patient's clinic indicates it.